Hereditary gingival fibromatosis – a case report and management using a novel surgical technique

Resumo

Introduction: Hereditary gingival fibromatosis (HGF) is a rare
condition presenting varied degrees of gingival enlargement. HGF
can present as an isolated entity or as part of a syndrome. Current
literatures report a defect in the Son of sevenless-1 gene (SOS1) on chromosome 2p21-p22 (HGF1) as a possible cause of this
condition. Case report: A case of a 16-year-old female is reported
who presented generalized extensive gingival overgrowth, involving
the maxillary and mandibular arches covering almost two thirds to
three quarters of all teeth. Diagnosis of HGF was substantiated by
the patient’s clinical features, family history and histopathological
examination. Treatment was excision of the gingival tissue by a
modified gingivectomy technique with both manual instrumentation
and electrosurgery. The postoperative course was uneventful and the
patient’s aesthetic concerns were addressed. Post-surgical follow-up
after 18 months demonstrated no recurrence. Conclusion: Hereditary
gingival fibromatosis stands apart from other gingival enlargements
in the varied treatment options available and the nature of recurrence
post treatment. There is no consensus among authors related to the
mode of treatment. Here, in this present case report we highlight
a novel surgical technique to deal with the extensive nature of
enlargement seen in HGF cases.